Other necrotizing vasculopathies
Other necrotizing vasculopathies
M31 is a header (parent) code in the ICD-10-CM hierarchy. It is not billable for claim submission. Use one of the billable child codes listed below.
Billable codes in this category
Each of the codes below is billable. Choose the one that most accurately describes the patient's diagnosis.
M31.0 classifies hypersensitivity angiitis, an immune-mediated necrotizing vasculopathy of small vessels, and explicitly includes Goodpasture's syndrome (anti-glomerular basement membrane disease) as an applicable condition under this code.
M31.2 classifies lethal midline granuloma, a rare and destructive necrotizing vasculopathy characterized by progressive inflammation, ulceration, and tissue destruction centered on the midline facial structures — primarily the nose, sinuses, and hard palate.
Chronic granulomatous large-vessel vasculitis targeting the aorta and its primary branches, producing progressive stenosis, occlusion, and aneurysm formation — classified under ICD-10-CM as Takayasu arteritis (aortic arch syndrome).
M31.5 identifies giant cell arteritis (GCA) occurring concurrently with polymyalgia rheumatica (PMR) — a combined presentation requiring documentation of both conditions to justify this code over M31.6.
Giant cell arteritis (GCA) without concurrent polymyalgia rheumatica — a granulomatous large-vessel vasculitis affecting the aorta and its branches, most commonly the temporal and cranial arteries, in patients typically aged 50 or older.
M31.7 identifies microscopic polyangiitis (MPA), a systemic ANCA-associated vasculitis targeting small vessels — and occasionally medium vessels — with a predilection for renal and pulmonary involvement.
M31.8 captures necrotizing vasculopathies that are specifically identified by the clinician but do not map to any individually named subcategory within the M31 parent block — including hypocomplementemic vasculitis and septic vasculitis.
Necrotizing vasculopathy of unspecified type — inflammatory destruction of blood vessel walls without a more specific M31 subcategory identified in the documentation.