M30.2 classifies juvenile polyarteritis — a pediatric-onset necrotizing vasculitis of medium-sized arteries that mirrors polyarteritis nodosa (M30.0) but occurs in children and adolescents.
Verified May 8, 2026 · 4 sources ↓
- Status
- Billable
- Chapter
- 13
- Related CPT
- 5
- Region
- General
Documentation tips
What should appear in the chart to support M30.2.
Source · Editorial brief grounded in 4 cited references ↓
- Provider must explicitly document 'juvenile polyarteritis' — a generic 'vasculitis' or 'polyarteritis' entry without age qualifier does not support M30.2 over M30.0.
- Record the patient's age at onset and at the encounter; the 'juvenile' designation requires pediatric-onset disease and should be reflected in the clinical note.
- Document all organ-system complications (renal, cardiac, neurologic, musculoskeletal) separately so complicating conditions can be coded to raise DRG severity from 547 to 546 or 545.
- If imaging (angiography, MRI/MRA) or biopsy findings support the diagnosis, reference those results in the note — they substantiate medical necessity and anchor the diagnosis against audit.
- Distinguish juvenile polyarteritis (M30.2) from microscopic polyarteritis (M31.7) in the documentation; the two are mutually exclusive under the M30 Excludes1 note.
Related CPT procedures
Procedure codes commonly billed with M30.2. Linking the right diagnosis to the right procedure is what establishes medical necessity.
Source · CMS LCDs · AAOS specialty guidance · claims-pattern analysis
Common coding pitfalls
The recurring mistakes coders make with M30.2 and adjacent codes.
Source · Editorial brief grounded in CDC ICD-10-CM tabular guidance, AAOS coding references, and cited references ↓
- Assigning M30.0 (polyarteritis nodosa) instead of M30.2 when the patient is a child — the Alphabetic Index explicitly routes juvenile cases to M30.2, not M30.0.
- Coding M31.7 (microscopic polyarteritis) for a documented juvenile polyarteritis case — M31.7 is Excludes1 from M30, meaning it cannot be used simultaneously with any M30.x code.
- Using an unspecified vasculitis code when the provider has clearly documented juvenile polyarteritis — this loses specificity and may trigger a medical necessity query.
- Failing to capture comorbid manifestations (e.g., hypertension, renal involvement) as additional codes, leaving DRG severity understated and reimbursement at the lowest tier (DRG 547).
Clinical context
Source · Editorial summary grounded in 4 cited references ↓
M30.2 is the billable code for juvenile polyarteritis, a rare systemic vasculitis affecting medium-caliber arteries in pediatric patients. It sits under parent code M30 (Polyarteritis nodosa and related conditions) within the M30–M36 block of systemic connective tissue disorders. The ICD-10-CM Alphabetic Index routes 'Polyarteritis nodosa, juvenile' directly to M30.2, confirming this is the correct landing code — not M30.0 (adult polyarteritis nodosa) or M31.7 (microscopic polyarteritis, which is explicitly excluded from M30).
In an orthopedic or musculoskeletal coding context, M30.2 appears when a pediatric patient presents with joint pain, limb ischemia, or soft-tissue manifestations secondary to underlying vasculitis. The treating provider — typically a pediatric rheumatologist — must document the juvenile polyarteritis diagnosis explicitly; coders cannot infer it from symptoms alone. If the provider documents only 'vasculitis, unspecified' without specifying juvenile polyarteritis, M30.2 is not appropriate.
MS-DRG v42.0 groups M30.2 into DRGs 545, 546, or 547 (Connective Tissue Disorders with MCC, CC, or without CC/MCC, respectively), so accurate capture of complicating conditions in the claim directly affects reimbursement tier. Always code any documented organ-system manifestations separately when they are not integral to the vasculitis itself, per ICD-10-CM syndrome coding guidance.
Sibling codes
Other billable codes under M30 (laterality / anatomic variants).
Frequently asked questions
Source · Generated from the editorial pipeline, verified against 4 cited references ↓
01Can M30.2 be used for an adult patient whose juvenile polyarteritis was diagnosed in childhood?
02Is M30.2 ever used alongside M31.7 (microscopic polyarteritis)?
03What DRGs does M30.2 map to, and what affects which tier the claim lands in?
04Can a coder assign M30.2 based on symptoms alone if the provider hasn't explicitly stated 'juvenile polyarteritis'?
05Does M30.2 require a 7th-character extension?
06How does M30.2 differ from M30.0 (polyarteritis nodosa)?
07Are there any orthopedic-specific CPT procedures commonly billed with M30.2?
Sources & references
Editorial content was developed using the following public sources. Last verified May 8, 2026.
- 01CDC ICD-10-CM Tabular List 2026 — code M30.2
- 02icd10data.comhttps://www.icd10data.com/ICD10CM/Codes/M00-M99/M30-M36/M30-/M30.2
- 03stacks.cdc.govhttp://stacks.cdc.gov/view/cdc/158747
- 04cms.govhttps://www.cms.gov/medicare/coding-billing/icd-10-codes
Mira AI Scribe
The Mira AI Scribe captures the patient's age at symptom onset, the provider's explicit 'juvenile polyarteritis' diagnosis label, and any documented organ-system involvement (renal, cardiac, musculoskeletal) from the encounter note. It also flags angiographic or biopsy findings cited in the record. Capturing these elements prevents the encounter from being coded to a nonspecific vasculitis code or misdirected to M30.0, and ensures complicating conditions are coded to push DRG assignment above the base tier.
See how Mira captures M30.2 documentation