M30.0 identifies classic polyarteritis nodosa (PAN), a systemic necrotizing vasculitis affecting medium-sized muscular arteries, distinct from microscopic polyangiitis and other related vasculitides.
Verified May 8, 2026 · 5 sources ↓
- Status
- Billable
- Chapter
- 13
- Related CPT
- 0
- Region
- Multi-region
Documentation tips
What should appear in the chart to support M30.0.
Source · Editorial brief grounded in 5 cited references ↓
- Confirm the physician has explicitly documented 'polyarteritis nodosa' or an indexed synonym (panarteritis nodosa, periarteritis nodosa, panangiitis, Kussmaul's disease) — generic 'vasculitis' does not map to M30.0.
- Document any secondary manifestations separately: peripheral polyneuropathy (G62.9), myopathy (G72.9), or organ-specific ischemic findings, so additional codes can be assigned.
- Record diagnostic workup that supports PAN — biopsy findings, angiographic abnormalities, or serologic results — to substantiate medical necessity on audit.
- Distinguish clinically between classic PAN (medium vessel, ANCA-negative) and microscopic polyangiitis (small vessel, often ANCA-positive) in the documentation, since the two map to different codes (M30.0 vs. M31.7) and cannot be coded together.
- If the encounter involves a rheumatology or orthopedic consultation for joint or muscle symptoms attributable to PAN, document PAN as the underlying cause linking it to the musculoskeletal presentation.
Common coding pitfalls
The recurring mistakes coders make with M30.0 and adjacent codes.
Source · Editorial brief grounded in CDC ICD-10-CM tabular guidance, AAOS coding references, and cited references ↓
- Using M30 (the non-billable parent) instead of M30.0 — M30 will be rejected for reimbursement; always code to the specific child code.
- Coding M30.0 alongside M31.7 (microscopic polyangiitis) — a Type 1 Excludes note at category M30 prohibits simultaneous use; these two conditions are mutually exclusive in ICD-10-CM.
- Defaulting to M30.0 when documentation actually describes Churg-Strauss syndrome with lung involvement — that presentation belongs to M30.1, not M30.0.
- Omitting secondary codes for neurologic or myopathic manifestations of PAN, which leaves the full clinical picture uncoded and can underrepresent severity for risk-adjustment purposes.
Clinical context
Source · Editorial summary grounded in 5 cited references ↓
M30.0 is the correct code for classic polyarteritis nodosa — a necrotizing inflammation of medium-caliber arteries that can cause ischemic damage to multiple organ systems including peripheral nerves, kidneys, skin, joints, and musculoskeletal structures. It is also indexed under synonyms including panarteritis nodosa, periarteritis nodosa, panangiitis, and Kussmaul's disease. When PAN produces peripheral polyneuropathy, code G62.9 may be added; when it produces myopathy, consider additional coding with G72.9.
This code sits under parent category M30 (Polyarteritis nodosa and related conditions). Do not use M30.0 when microscopic polyarteritis is documented — that condition maps exclusively to M31.7, which carries a Type 1 Excludes note at the M30 category level, prohibiting simultaneous use with any M30 code. Similarly, if lung involvement is documented alongside vasculitis features, evaluate M30.1 (Churg-Strauss) rather than M30.0.
PAN is not a primary orthopedic diagnosis, but it appears in orthopedic and rheumatologic practice when patients present with vasculitis-driven joint pain, myopathy, or peripheral neuropathy. Coders documenting PAN in these settings should capture any secondary musculoskeletal or neurologic manifestations with appropriate additional codes. The parent code M30 is non-billable; M30.0 is the specific, billable option for classic PAN.
Sibling codes
Other billable codes under M30 (laterality / anatomic variants).
Frequently asked questions
Source · Generated from the editorial pipeline, verified against 5 cited references ↓
01Is M30 billable, or do I need M30.0?
02Can I code M30.0 and M31.7 on the same claim?
03What code covers polyarteritis with lung involvement?
04PAN caused my patient's peripheral neuropathy — how do I code that?
05What synonyms index to M30.0 in ICD-10-CM?
06Is M30.0 appropriate when a patient has juvenile polyarteritis?
07Does M30.0 require a 7th character extension?
Sources & references
Editorial content was developed using the following public sources. Last verified May 8, 2026.
- 01CDC ICD-10-CM Tabular List 2026 (effective October 1, 2025)
- 02icd10data.comhttps://www.icd10data.com/ICD10CM/Codes/M00-M99/M30-M36/M30-/M30.0
- 03icd10data.comhttps://www.icd10data.com/ICD10CM/Codes/M00-M99/M30-M36/M30-/M30
- 04aapc.comhttps://www.aapc.com/codes/icd-10-codes/M30.0
- 05autoicdapi.comhttps://autoicdapi.com/icd10-to-icd11/M30.0
Mira AI Scribe
Mira captures the physician's documented diagnosis of polyarteritis nodosa along with any indexed synonyms (panarteritis, periarteritis, Kussmaul's disease), distinguishes classic PAN from microscopic polyangiitis based on vessel size and ANCA status noted in the encounter, and flags secondary neurologic or myopathic manifestations for additional coding — preventing undercoding of systemic involvement and blocking the M30 non-billable parent from slipping through to claim submission.
See how Mira captures M30.0 documentation